Benji Exam 1

1. The different forms or values of a gene that an individual may possess (e.g., blue eyes, vs. brown eyes) is called ___________
a. a gene
b. an allele
c. a chromosome
d. DNA

2. In both parents are carriers (each one with an abnormal recessive gene), their children have a ______ chance of having the disorder.
A. 50 %
B. 75%
C. 25 %
D. 100 %

4. An abnormally small pinna is called _______________.
A. Anotia
B. Aplasia
C. Microtia
D. Aural Stenosis

5. Aural atresia will result in a __________________ hearing loss.
A. conductive
B. mixed
C. sensorineural
d. none of the above

6. An abnormal bony growth on the ear canal wall:
A. cerumen
B. otitis media
C. exostosis
D. external otitis

3. This most common form of genetic hearing loss is _____________________
A. sex-linked, and non-syndromic
B. autosomal dominant, and syndromic
C. autosomal recessive, and syndromic
D. autosomal recessive, and non-syndromic

An infection in the outer ear (AKA swimmers ear):
A. exostosis
B. cerumen
C. otitis media
D. external otitis

8. Painful blisters on the TM:
A. Bullous Mryingitis
B. Tympanosclerosis
C. otitis media with effusion
D. serous otitis media

9. Tympanosclerosis usually results in:
A. no hearing loss,
B. a significant conductive hearing loss
C. damage to the outer hair cells
D. a sensorineural hearing loss

10. Tympanic membrane perforations can be caused by:
a. foreign objects (Q-tips)
b. barotrauma
c. middle ear infections
d. a and c
e. all of the above

11. When fluid accumulates in the middle ear space, but is not infected:
A. glomous tumor
B. otosclerosis
C. cholestoetoma
D. mastoiditis
E. acute otitis media
F. otitis media with effusion

12. An accumulation of keratin and skin debris in the middle ear:
A. otosclerosis
B. acute otitis media
C. otitis media with effusion
D. cholestoetoma
E. mastoiditis
F. glomous tumor

13. Results in pulsing tinnitus:
A. acute otitis media
B. cholestoetoma
C. otitis media with effusion
D. glomous tumor
E. mastoiditis
F. otosclerosis

14. Spongy bone that grows and hardens on the ossicles, preventing them from moving properly:
A. mastoiditis
B. glomous tumor
C. otitis media with effusion
D. cholestoetoma
E. otosclerosis
F. acute otitis media

15. Disorders that prevent sound from being transmitted to the cochlea efficiently result in a ____________ hearing loss:
A. outer hair cell
B. conductive
C. mixed
D. sensorineural

16. Disorders originating from the cochlea or auditory nerve result in a ____________ hearing loss:
A. central
B. mixed
C. conductive
D. sensorineural

17. Occurs when there is a conductive and sensorineural hearing loss.
A. mixed hearing loss
B. central hearing loss
C. Ischemia
D. meniers disease

18. Which disorder is associated with eyes that are 2 different colors, white forelock, and sensorineural hearing loss?
A. Alport syndrome
B. Kippel-Feil syndrome
C. Neurofibromatosis 2
D. Waardenberg syndrome

19. Which disorder is associated with excessive endolymphatic fluid pressure?
A. Goldenhar’s syndrome
B. Alport syndrome
C. Waardenberg syndrome
D. Menier’s Disease

20. Perception of sound when there is no external sound present is called:
A. Tinnitus
B. Conductive hearing loss
C. Perilymphatic fistula
D. Endolymphatic hydrops

21. Tympanic membrane perforations:
a. can heal on their own without any treatment
b. are repaired with surgery
c. can cause auditory neuropathy
d. both a and b

22. A leak of fluid from a round window or oval window rupture:
A. Presbycusis
B. Auditory Neuropathy
C. Perilymphatic fistula
D. Endolymphatic hydrops

23. A synchronous signal is not coded by the hearing system:
A. Tinnitus
B. Conductive hearing loss
C. Perilymphatic fistula
D. Auditory Neuropathy

24. Vestibular schwannoma tumors are usually unilateral, but bilateral cases sometimes occur in patients with ________________.
A. Meniers Disease
B. Waardenberg syndrome
C. Pagets Disease
D. Neurofibromatosis 2 (NF2)

25. Hearing loss due to aging:
A. Otosclerosis
B. Presbycusis
C. Meniers Disease
D. Hypoxia

26. Continued exposure to sounds louder than _______ dB SPL can result in permanent noise induce hearing loss.
A. 80
B. 60
C. 100
D. 120

27. Initially, meneir’s disease presents with __________________
A. high-frequency sensorineural hearing loss
B. high-frequency conductive hearing loss
C. low-frequency conductive hearing loss
D. low-frequency sensorineural hearing loss

28. Hearing loss due to noise exposure initially causes the greatest hearing loss at ________________ , and later spreads to other frequencies as exposure continues.
A. 8,000 Hz
B. 2,000 Hz
C. 4,000 Hz
D. 1,000 Hz

29. The auditory cortex is located in the __________ lobe.
A. temporal
B. occipital
C. frontal
D. parietal

30. Wernicke’s area is associated with ______________.
A. musical analysis
B. motor control of speech
C. noise analysis
D. speech analysis

31. Broca’s area is associated with ______________.
A. noise analysis
B. motor control of speech
C. musical analysis
D. speech analysis

32. Patients with auditory processing disorder have trouble ______________.
a. hearing soft sounds
b. with speech understanding in noise
c. dichotic processing
d. b and c

True or False

33. Ear candles are an effective method of cerumen removal.
34. A father will pass his mitochondrial DNA on to his sons.

35. Genetics are the only cause for congenital hearing loss.

True or False

Bacterial Meningitis can cause a severe to profound conductive hearing loss.

True or False

Patients with auditory neuropathy have normal outer hair cell function.

True or False

Surgical reconstruction of the pinna is relatively quick, and can be completed in a single surgery.

True or False